CT of sebaceous nevus syndrome (Jadassohn disease).

The sebaceous nevus, a congenital sk in disease, was first described in 1895 by Jadassohn [1] and later became known as the organoid nevus syndrome within the grouping of the phacomatoses [2]. In 1957 , Schimmelpenning [3] described its assoc iation with central nervous system, skeletal, and eye lesions. In 1962, Feuerstein and Mims [4] reported a case with epi lepsy and mental retardation . In the last 10 years , 19 cases presenting with a wide variety of symptomatology have been reported in the literature [5-1 9]. We report a case of Jadassohn disease in which, to the best of our knowledge, both conventional ax ial and direct sag ittal computed tomography (CT) were performed for the first time.